Juanma Fernández-Costa

Senior Research Scientist

Publications


Fatty Hepatocytes Induce Skeletal Muscle Atrophy In Vitro: A New 3D Platform to Study the Protective Effect of Albumin in Non-Alcoholic Fatty Liver


F. De Chiara, A. Ferret-Miñana, J.M. Fernández-Costa, A. Senni, R. Jalan, J. Ramón-Azcón

Biomedicines, vol. 10, 2022


Training-on-a-Chip: A Multi-Organ Device to Study the Effect of Muscle Exercise on Insulin Secretion in Vitro


J.M. Fernández-Costa, M.A. Ortega, J. Rodríguez-Comas, G. Lopez-Muñoz, J. Yeste, L. Mangas-Florencio, M. Fernández-González, E. Martin-Lasierra, A. Tejedera-Villafranca, J. Ramon-Azcon

Advanced Materials Technologies, 2022


Xeno-free bioengineered human skeletal muscle tissue using human platelet lysate-based hydrogels


X. Fernández-Garibay, M. Gómez-Florit, R.M.A. Domingues, M.E. Gomes, J.M. Fernández-Costa, J. Ramón-Azcón

Biofabrication, vol. 14, 2022


Organs-on-Chips: Trends and Challenges in Advanced Systems Integration


S. Mughal, G.A. López-Muñoz, J.M. Fernández-Costa, A. Cortés-Reséndiz, F. De Chiara, J. Ramón-Azcón

Advanced Materials Interfaces, vol. 9, 2022


Inhibition of autophagy rescues muscle atrophy in a LGMDD2 Drosophila model


Á. Blázquez-Bernal, J.M. Fernandez-Costa, A. Bargiela, R. Artero

FASEB Journal, vol. 35, 2021


Preclinical characterization of antagomiR-218 as a potential treatment for myotonic dystrophy


E. Cerro-Herreros, I. González-Martínez, N. Moreno, J. Espinosa-Espinosa, J.M. Fernández-Costa, A. Colom-Rodrigo, S.J. Overby, D. Seoane-Miraz, J. Poyatos-García, J.J. Vilchez, A. López de Munain, M.A. Varela, M.J. Wood, M. Pérez-Alonso, B. Llamusí, R. Artero

Molecular Therapy - Nucleic Acids, vol. 26, 2021, pp. 174-191


Bioengineered in vitro skeletal muscles as new tools for muscular dystrophies preclinical studies


J.M. Fernández-Costa, X. Fernández-Garibay, F. Velasco-Mallorquí, J. Ramón-Azcón

Journal of Tissue Engineering, vol. 12, 2021


Bioengineered in vitro 3D model of myotonic dystrophy type 1 human skeletal muscle


X. Fernández-Garibay, M.A. Ortega, E. Cerro-Herreros, J. Comelles, E. Martínez, R. Artero, J.M. Fernández-Costa, J. Ramón-Azcón

Biofabrication, vol. 13, 2021


Plasmonic nanocrystals on polycarbonate substrates for direct and label-free biodetection of Interleukin-6 in bioengineered 3D skeletal muscles


G.A. Lopez-Munõz, J.M. Fernández-Costa, M.A. Ortega, J. Balaguer-Trias, E. Martin-Lasierra, J. Ramón-Azcón

Nanophotonics, vol. 10, 2021, pp. 4477-4488


Rabphilin involvement in filtration and molecular uptake in Drosophila nephrocytes suggests a similar role in human podocytes


E. Selma-Soriano, B. Llamusi, J.M. Fernández-Costa, L.L. Ozimski, R. Artero, J. Redón

DMM Disease Models and Mechanisms, vol. 13, 2020


New volumetric CNT-doped gelatin-cellulose scaffolds for skeletal muscle tissue engineering


F. Velasco-Mallorquí, J.M. Fernández-Costa, L. Neves, J. Ramón-Azcón

Nanoscale Advances, vol. 2, 2020, pp. 2885-2896


MiR-23b and miR-218 silencing increase Muscleblind-like expression and alleviate myotonic dystrophy phenotypes in mammalian models


E. Cerro-Herreros, M. Sabater-Arcis, J.M. Fernandez-Costa, N. Moreno, M. Perez-Alonso, B. Llamusi, R. Artero

Nature Communications, vol. 9, 2018


Myotonic dystrophy: candidate small molecule therapeutics


P. Konieczny, E. Selma-Soriano, A.S. Rapisarda, J.M. Fernandez-Costa, M. Perez-Alonso, R. Artero

Drug Discovery Today, vol. 22, 2017, pp. 1740-1748


Derepressing muscleblind expression by miRNA sponges ameliorates myotonic dystrophy-like phenotypes in Drosophila


E. Cerro-Herreros, J.M. Fernandez-Costa, M. Sabater-Arcis, B. Llamusi, R. Artero

Scientific Reports, vol. 6, 2016


Six serum miRNAs fail to validate as myotonic dystrophy type 1 biomarkers


J.M. Fernandez-Costa, B. Llamusi, A. Bargiela, M. Zulaica, M.C. Alvarez-Abril, M. Perez-Alonso, A.L. De Munain, A. Lopez-Castel, R. Artero

PLoS ONE, vol. 11, 2016


Increased autophagy and apoptosis contribute to muscle atrophy in a myotonic dystrophy type 1 Drosophila model


A. Bargiela, E. Cerro-Herreros, J.M. Fernandez-Costa, J.J. Vilchez, B. Llamusi, R. Artero

DMM Disease Models and Mechanisms, vol. 8, 2015, pp. 679-690


Expanded CTG repeats trigger miRNA alterations in Drosophila that are conserved in myotonic dystrophy type 1 patients


J.M. Fernandez-Costa, A. Garcia-Lopez, S. Zuñiga, V. Fernandez-Pedrosa, A. Felipo-Benavent, M. Mata, O. Jaka, A. Aiastui, F. Hernandez-Torres, B. Aguado, M. Perez-Alonso, J.J. Vilchez, A. Lopez de Munain, R.D. Artero

Human Molecular Genetics, vol. 22, 2013, pp. 704-716


Muscleblind, BSF and TBPH are mislocalized in the muscle sarcomere of a Drosophila myotonic dystrophy model


B. Llamusi, A. Bargiela, J.M. Fernandez-Costa, A. Garcia-Lopez, R. Klima, F. Feiguin, R. Artero

DMM Disease Models and Mechanisms, vol. 6, 2013, pp. 184-196


Alternative splicing regulation by Muscleblind proteins: From development to disease


J.M. Fernandez-Costa, M.B. Llamusi, A. Garcia-Lopez, R. Artero

Biological Reviews, vol. 86, 2011, pp. 947-958


A conserved motif controls nuclear localization of Drosophila Muscleblind


J.M. Fernandez-Costa, R. Artero

Molecules and Cells, vol. 30, 2010, pp. 65-70


A GFP-tagged muscleblind C protein isoform reporter construct


M. Pascual, L. Monferrer, J.M. Fernandez-Costa, A. Bargiela, R. Artero, B. Llamusi

Fly, vol. 4, 2010, pp. 333-337


Drosophila muscleblind is involved in troponin T alternative splicing and apoptosis


M. Vicente-Crespo, M. Pascual, J.M. Fernandez-Costa, A. Garcia-Lopez, L. Monferrer, M.E. Miranda, L. Zhou, R.D. Artero

PLoS ONE, vol. 3, 2008




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